Overview
Desmoplastic small round cell tumor (DSRCT) is a rare type of soft tissue sarcoma. In DSRCT, fast-growing tumors develop in your peritoneum — the membrane that lines the inside of your abdomen and your pelvis.
Anyone may develop DSRCT, but it typically affects men and people assigned male at birth (AMAB) between ages 20 and 30. Healthcare providers have treatments that can put the condition into remission, but it often comes back (recurs).
How rare is DSRCT?
DSRCT is a very rare condition, affecting about 1 in 1 billion people worldwide since researchers first identified it in 1989.
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